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Stenosis of the cervical canal in craniodiaphyseal dysplasia

Department of Orthopaedics, Charing Cross Hospital, Fulham Palace Road, London W6 8RF, UK.

V. J. Laheri, MS Orth, Professor and Head

Department of Orthopaedics, The Seth GS Medical College & The King Edward VII Memorial Hospital, Mumbai 400012, India.

Correspondence should be sent to Mr S. Naique.

Craniodiaphyseal dysplasia (CDD) is a rare sclerosing bone disorder, the severity of which depends on its phenotypic expression. Hyperostosis can cause progressive foraminal stenosis leading to palsy of cranial nerves, epilepsy and mental retardation. We report the only case of CDD in an adult, with stenosis of the cervical canal leading to quadriparesis as a late complication of hyperostosis, and describe the problems associated with its treatment. Although the syndrome is rare, its pathophysiological and therapeutic considerations may be applicable to the management of stenosis of the spinal canal in other hyperostotic bone disorders.